Author/Editor | Zver, Samo; Noč, Marko; Horvat, Matija; Ponikvar, Rafael | |
Title | Trombotična trombocitopenična purpura - prikaz kliničnega primera | |
Translated title | Thrombotic thrombocytopenic purpura with case report | |
Type | članek | |
Source | Zdrav Vestn | |
Vol. and No. | Letnik 66, št. 4 | |
Publication year | 1997 | |
Volume | str. 187-9 | |
Language | slo | |
Abstract | Background. We present a patient with thrombotic thrombocytopenic purpura, which involved different organs and, especially kidneys, lung and central nervous system. In addition to mechanical ventilation and haemodialysis, Be was treated with plasma exchange, glucocorticoids and prostacyclin. Conclusions. The treatment was successfull and the patient has been in good health for three months. A short review of the literature on thrombotic thrombocytopenic purpura and different treatment modalities is also provided. | |
Summary | Izhodišča. Opisan je primer bolnika s trombotično trombocitopenično purpuro. Bolezen je prizadela vse organske sisteme, predvsem pa ledvici, pljuča in osrednje živčevje. Poleg razdihavanja (umetne ventilacije) in hemodialize smo bolnika zdravili z izmenjavo plazme, glukokortikoidi in prostaciklinom. Zaključki. Zdravljenje je bilo uspešno in bolnik normalno živi že tri mesece. Povzet je tudi kratek pregled literature o tej sicer redki bolezni in vrstah zdravljenja. | |
Descriptors | PURPURA, THROMBOTIC THROMBOCYTOPENIC ADULT |