Author/Editor     Zver, Samo; Noč, Marko; Horvat, Matija; Ponikvar, Rafael
Title     Trombotična trombocitopenična purpura - prikaz kliničnega primera
Translated title     Thrombotic thrombocytopenic purpura with case report
Type     članek
Source     Zdrav Vestn
Vol. and No.     Letnik 66, št. 4
Publication year     1997
Volume     str. 187-9
Language     slo
Abstract     Background. We present a patient with thrombotic thrombocytopenic purpura, which involved different organs and, especially kidneys, lung and central nervous system. In addition to mechanical ventilation and haemodialysis, Be was treated with plasma exchange, glucocorticoids and prostacyclin. Conclusions. The treatment was successfull and the patient has been in good health for three months. A short review of the literature on thrombotic thrombocytopenic purpura and different treatment modalities is also provided.
Summary     Izhodišča. Opisan je primer bolnika s trombotično trombocitopenično purpuro. Bolezen je prizadela vse organske sisteme, predvsem pa ledvici, pljuča in osrednje živčevje. Poleg razdihavanja (umetne ventilacije) in hemodialize smo bolnika zdravili z izmenjavo plazme, glukokortikoidi in prostaciklinom. Zaključki. Zdravljenje je bilo uspešno in bolnik normalno živi že tri mesece. Povzet je tudi kratek pregled literature o tej sicer redki bolezni in vrstah zdravljenja.
Descriptors     PURPURA, THROMBOTIC THROMBOCYTOPENIC
ADULT