Author/Editor     Pahor, Artur
Title     Wegenerjeva granulomatoza - diagnostični izziv: prikaz iz klinične prakse
Translated title     Wegener's granulomatosis - diagnosis challenge: case report
Type     članek
Source     Med Razgl
Vol. and No.     Letnik 38, št. Suppl 1
Publication year     1999
Volume     str. 23-9
Language     slo
Abstract     A patient with Wegener's granulomatosis with only eye and articular involvement for more than a year is presented in this article. Diagnose was established when patient developed systemic clinical signs and involvement of visceral organs especially lung, kidney and heart. The most important for definitive diagnose were presence of antineutrophil cytoplasmic antibodies in classic pattern and renal biopsy. Therapeutic procedures which resulted in complete remission of disease are described.
Summary     V prispevku je predstavljen bolnik z Wegenerjevo granulomatozo, ki se je več kot leto dni kazala le z očesnimi in sklepnimi kliničnim znaki in ostala neprepoznana do pojava sistemskih znakov in prizadetosti notranjih organov, zlasti pljuč, ledvic in srca. V diagnostiki sta bila odločujoči prisotnost protiteles proti citoplazmi nevtrofilcev v klasičnem vzorcu ter ledvična biopsija. Opisani sta tudi metodi zdravljenja, ki sta privedli do popolne ozdravitve bolezni.
Descriptors     WEGENER'S GRANULOMATOSIS
ANTIBODIES, ANTINEUTROPHIL CYTOPLASMIC