Author/Editor		Ferlan-Marolt, V; Štepec, S; Luzar, B
Title		Fulminant Wilsonian hepatitis unmasked by disease progression
Type		članek
Source		Rev Ser Hepatitis
Vol. and No.		, št. 3
Publication year		2000
Volume		str. 17-9
Language		eng
Abstract		We report a patient with clinically indistinct manifestations of Wilson's disease of four week's duration who later presented with liver damage which rapidly progressed to death. During the prodromal period, the disease was not revealed on either clinical investigation of liver biopsy. However, fulminant hepatitis with hepatic failure followed. Liver damage was characterized by massive and confluent necrosis, severily inflamed fibrotic bridging, and areas where hepatocytes were overloaded with copper. A liver transplantation, as the theapy of choice, was planned but the liver lesion and associated renal insufficiency progressed so rapidly that the patient died before treatment could be carried out.
Descriptors		HEPATOLENTICULAR DEGENERATION ADULT FATAL OUTCOME