Avtor/Urednik     Malčić, I; Barišić, N; Brzović, Z; Pažanin, L; Senečić, I
Naslov     Cardiomyopathies in children with neuromuscular disorders
Tip     članek
Vir     Neurol Croat
Vol. in št.     Letnik 40, št. 4
Leto izdaje     1991
Obseg     str. 221-30
Jezik     eng
Abstrakt     In this paper eight patients with myogenic or neurogenic muscle disorders are presneted, in whom cardiomiopathy was also found. Six patients developed a dilated cardiomiopathy associated with neurogenic atrophies or progressive muscular dystrophy. In patients with Mb. Friedreich and HSNM type II together with the total dilatation of the septum hyperthrophy was observed and in patients with spinal muscular amyotrophy of scapuloperoneal type atriomyopathy dominated. In two patients with mitochondrial disorders a hypertrophic cardiomyopathy was found. One of them had mitochondrial encephalomyoneuropathy and the other mitochondrial encephalopathy with myoclonic epilepsy. In none of them a restrictive cardiomyopathy was found. From the presentation could be concluded that in neurogenic muscle diseases and progressive muscular dystrophy respectively most frequently dilated cardiomyopathies have been developed. Hypertrophic cardiomyopathies are usually found in children with mitochondrial disorders
Deskriptorji     CARDIOMYOPATHY, CONGESTIVE
CARDIOMYOPATHY, HYPERTROPHIC
NEUROMUSCULAR DISEASES
ELECTROCARDIOGRAPHY
INFANT
CHILD, PRESCHOOL
CHILD