Avtor/Urednik     Lučovnik, Miha; Vujasinović, Miroslav; Štabuc, Borut
Naslov     Dolgotrajno hranjenje bolnice s Cowdenovim sindromom po cevki skozi perkutano endoskopsko gastrostomo
Prevedeni naslov     Long-term feeding of a Cowden syndrome patient via percutaneous endoscopic gastrostomy tube
Tip     članek
Vir     Gastroenterolog
Vol. in št.     Letnik 9, št. 21
Leto izdaje     2005
Obseg     str. 16-8
Jezik     slo
Abstrakt     'I'he appropriate use of long-term enteral nutrition is often debated. Feeding by gastrostomy tube offers many advantages over other forms of enteral and parenteral nutrition. Since 1980 when percutaneous endoscopic gastrostomy (PEG) was first described, it has become the method of choice for gastrostomy tube placement. Cowden's syndrome is an autosomal dominant disease characterised by multiple hamartomas, mostly in the intestinal tract and skin with increased risk of breast, thyroid and some other forms of cancer. We present a patient with Cowden's syndrome whose only enteral nutrient and fluid intake has been through PEG for the last eight years.
Izvleček     Dolgotrajno enteralno hranjenje je predmet mnogih razprav. Enteralno hranjenje po cevi skozi gastrostorno ima številne prednosti pred drugimi oblikami enteralnega in pred parenteralnim hranjenjem. Od leta 1980, ko je bila prvič opisana perkutana endoskopska gastrostomija (PEG), je postala endoskopska izdelava gastrostome in postavitev prehranjevalne cevi metoda izbire. Cowdenov sindrom je avtosomsko dominantna dedna bolezen za katero so značilni multipli hamartomi, predvsem po koži in v celotnem prebavnem traktu, in večja ogroženost z rakom dojke, ščitnice in z nekaterimi drugimi neoplazmami. Opisujemo primer, ko se bolnica zaradi masivne polipoze ust, žrela in požiralnika že osem let hrani izključno po PEG.
Deskriptorji     HAMARTOMA SYNDROME, MULTIPLE
GASTROSTOMY
ENTERAL NUTRITION
MIDDLE AGE