Avtor/Urednik     Šujica, Ana; Pagon, Andreja; Bartenjev, Igor
Naslov     A case of segmental form of type 1 mosaic Darier’s disease
Tip     članek
Vol. in št.     Letnik 31, št. suppl.
Leto izdaje     2022
Obseg     str. S31-S35
ISSN     1318-4458 - Acta dermatovenerologica Alpina, Panonnica et Adriatica
Jezik     eng
Abstrakt     Darier’s disease is a rare genetic disorder with autosomal dominant inheritance. It is characterized by hyperkeratotic papules in seborrheic areas. Associated abnormalities include nail abnormalities and changes in the mucous membranes. Exacerbation of the disease occurs with exposure to high temperatures, sun, and sweating, resulting in a worsening clinical picture in summer months. The unilateral zosteriform pattern is a rare variant that is clinically manifested by a unilateral outbreak of erythema- tous keratotic papules without any other associated symptoms. Here we present a 52-year-old male with a zosteriform pattern of Darier’s disease. We also discuss the most important clinical and pathohistological characteristics of the disease and various treatment options.
Proste vsebinske oznake     Darierjeva bolezen
akantolitična dermatoza
delna abrazija
Darier’s disease
acantholytic dermatosis
partial abrasion