Avtor/Urednik | Potušek-Kuhar, K; Logar-Car, G; Mlinarič, V | |
Naslov | Primarni sklerozirajoči holangitis pri otroku | |
Prevedeni naslov | Primary sclerosing cholangitis at the children | |
Tip | članek | |
Vir | Slov Pediatr | |
Vol. in št. | Letnik 4, št. 3-4 | |
Leto izdaje | 1997 | |
Obseg | str. 54-6 | |
Jezik | slo | |
Abstrakt | The article describes the patient with sclerosing cholangitis as well as chronic inflammatory bowel disease. The epidemiology, pathogenesis, clinical picture, diagnostics, prognosis and treatment of the disease are described. A 13-year boy was diagnosed to have chronic inflammatory bowel disease. Because of recuring pathological liver tests and increased direct bilirubin the sclerosing cholangitis was suspected. Endoscopic retrograde cholangiopancreatography confirmed the diagnosis. The treatment included ursodeoxycholic acid which normalized liver tests. | |
Izvleček | Članek prikazuje bolnika s sklerozirajočim holangitisom, ki ima hkrati tudi kronično vnetno črevesno bolezen. Opisuje epidemiologijo, patogenezo, klinično sliko, prognozo in zdravljenje bolezni. Pri bolniku smo v starosti 13 let diagnosticirali kronično vnetno črevesno bolezen. Zaradi ponavljajočih se povišanih vrednosti jetrnih testov in direktnega bilirubina smo posumili na sklerozirajoči holangitis. Opravili smo endoskopsko retrogradno holangiopankreatografijo, ki je diagnozo potrdila. V zdravljenje smo vključili ursodeoksiholno kislino in jetrni testi so se normalizirali. | |
Deskriptorji | CHOLANGITIS, SCLEROSING INFLAMMATORY BOWEL DISEASES CHILD |