Avtor/Urednik		Flis, Vojko; Pavlovič, Milan; Matela, Jože
Naslov		Kronična venska insuficienca in kongenitalne anomalije
Prevedeni naslov		Chronic venous insufficiency and congenital anomalies
Tip		članek
Vir		Med Razgl
Vol. in št.		Letnik 39, št. Suppl 2
Leto izdaje		2000
Obseg		str. 129-33
Jezik		slo
Abstrakt		Chronic venous insufficiency accompanies a rare congenital and generalised mesodermal abnormality, called the Klippel-Trenaunay syndrome, which is characterised by macular vascular nevi, skeletal or soft tissue hypertrophy and venous varicosities. Other associated manifestations include deep venous anomalies, arteriovenous microfistulae, visceral hemangiomas and the Kasabach Merritt syndrome. In the related Parkes-Weber syndrome, high-output cardiac failure with macroarteriovenous fistula is frequently seen. Two patients with the Parkes-Weber and Klippel-Trenaunay syndrome are presented and their clinical pictures are reviewed.
Izvleček		Kronična venska insuficienca je spremljevalka redke prirojene bolezni mezoderma, za katero so značilni kožni hemangiomi, hipertrofija skeleta ali mehkih tkiv in varikozne vene. Gre za sindrom Klippel-Trenaunay. Pri bolnikih s to boleznijo lahko najdemo tudi anomalije na globokih venah, arterio-venske mikrofistule. Pogosto pa jo spremlja tudi sindrom Kasabach-Merrit. Pri sorodnem sindromu Parkes-Weber pogostokrat srečamo odpovedovanje srca in pojavljanje arterio-venskih makrofistul. Predstavljena sta bolnika s Parkes-Weberjevim sindromom in s sindromom Klippel-Trenaunay.
Deskriptorji		VENOUS INSUFFICIENCY VEINS CHRONIC DISEASE KLIPPEL-TRENAUNAY-WEBER SYNDROME ARTERIOVENOUS FISTULA HEMANGIOMA DIAGNOSIS, DIFFERENTIAL