Avtor/Urednik     Stopar, Simon; Podboj, Jernej
Naslov     Žilni tumorji nosu in obnosnih votlin
Prevedeni naslov     Vascular tumours of the nose and paranasal sinuses
Tip     članek
Vir     Med Razgl
Vol. in št.     Letnik 37, št. Suppl 3
Leto izdaje     2000
Obseg     str. 285-9
Jezik     slo
Abstrakt     Introduction: Lobular capillary hemangioma and cavernous hemangioma are the most frequent benign vascular tumours in the area of the nose and paranasal sinuses compared to malignant tumours (angiosarcoma, hemangiopericytoma, hemangioendothelioma), which are very rare. Patients: In the period 1990-1999, the Department of Otorhinolaryngology and Cervicofacial Surgery, University Medical Centre, Ljubljana, Slovenia, treated 36 patients with vascular tumours of the nose and paranasal sinuses, 30 of whom had benign and 6 had malignant tumours. There were 19 female and 17 male patients. Surgical treatment was performed on all the patients. A patient with a high grade angiosarcoma received postoperative chemotherapy, during which the tumour recurred. Later, radical surgery was performed in combination with radiotherapy. Two patients with hemangioendothelioma and one with a low grade angiosarcoma were treated with radiotherapy (TD 50-GO Gy), primarily postoperatively. Results: The tumour recurred in one of the patients with un intraosseal cavernous hemangioma and in one with a high grade angiosarcoma; it was surgically removed (radical excision). Following surgery using the sublabial approach, two patients experienced complications in the form of oroantral fistulae, which were surgically managed. The patients showed no signs of a relapse in the period from one to nine years after the completion of treatment. Discussion: Radical surgery is the most important part of treatment of benign and malignant vascular tumours of the nose and paranasal sinuses. In some cases, endoscopic surgery can be performed. The decision on additional therapy of malignant tumours with radiotherapy and/or chemotherapy depends on the histological diagnosis, grade of malignancy and radicality of the surgery. Endoscopic control examinations are performed regularly in the folow-up of our patients.
Izvleček     Uvod. Med žilnimi tumorji v področju nosu in obnosnih votlin prevladujejo benigni žilni tumorji (lobulirani kapilarni hemangiom, kavernozni hemangiom), medtem ko so maligni izredno redki (angiosarkom, hemangiopericitom, hemangioendoteliom). Naši bolniki. V obdobju od 1990 do 1999 smo na Kliniki za otorinolaringologijo in cervikofacialno kirurgijo v Ljubljani zdravili 36 bolnikov z žilnimi tumorji nosu in obnosnih votlin, med katerimi je 30 bolnikov imelo benigne in 6 maligne tumorje. Med njimi je bilo 19 žensk in 17 moških. Vsi so bili operirani. Bolnik z visoko malignim angiosarkomom je bil pooperacijsko zdravljen s kemoterapijo, med katero je prišlo do ponovitve. Angiosarkom je bil odstranjen s ponovno operacijo ki ji je sledilo še obsevanje. Dva bolnika s srednjemalignim hemangioendoteliomom in bolnica z nizkomalignim angiosarkomom so bili primarno pooperacijsko zdravljeni z obsevanjem (TD 50 oz. 60 Gy). Rezultati. Pri eni od bolnic z intraosalnim kavernoznim hemangiomom in pri bolniku z visoko malignim angiosarkomom je prišlo do ponovitve tumorja, ki smo ga radikalno odstranili. Pri dveh bolnikih so po posegu s sublabialnim pristopom nastale oroantralne komunikacije, ki smo jih kirurško oskrbeli. Vsi bolniki so po zdravljenju, od katerega je minilo od enega do devetih let, brez znakov ponovitve bolezni. Zaključki. Najpomembnejši del zdravljenja benignih in malignih žilnih tumorjev nosu in obnosnih votlin je radikalna operacija, ki je v nekaterih primerih lahko endoskopska. Odločitev o dodatnem zdravljenju malignih tumorjev z obsevanjem in/ali kemoterapijo je odvisna od radikalnosti operacije, vrste in stopnje malignosti tumorja. Po končanem zdravljenju so za sledenje bolnikov potrebne redne endoskopske kontrole.
Deskriptorji     NOSE NEOPLASMS
PARANASAL SINUS NEOPLASMS
VASCULAR NEOPLASMS
HEMANGIOMA, CAPILLARY
HEMANGIOMA, CAVERNOUS
HEMANGIOPERICYTOMA
HEMANGIOENDOTHELIOMA
RECURRENCE
POSTOPERATIVE CARE