Author/Editor     Salobir, Barbara; Možina, Hugon; Šabovič, Mišo; Praprotnik, Sonja; Turel, Matjaž; Terčelj-Zorman, Marjeta
Title     Predstavitev treh primerov bolnikov z neprepoznano pljučno arterijsko hipertenzijo
Translated title     Presentation of threee cases of patients with unrecognized pulmonary arterial hypertension
Type     članek
Source     Med Razgl
Vol. and No.     Letnik 42, št. Suppl 4
Publication year     2003
Volume     str. 65-7
Language     slo
Abstract     Pulmonary arterial hypertension is a chronic disease which appears as a primary disorder or in connection with other diseases, primarily chronic pulmonary thromboembolism and systemic connective tissue diseases. Because of an increase in blood pressure in the pulmonary circulation, there is a right-sided heart insufficiency and right-sided heart failure. This is almost always associated with a poor prognosis. It frequently remains unrecognized, even though it can be detected with simple diagnostic procedures such as - in addition to medical history and a detailed cfinical examination - ECG, chest x-ray and cardiac ultrasound. New findings on the etiopathogenesis of pulmonary arterial hypertension open new possibilities of treatment with drugs and/or surgical procedures, both for patients with primary pulmonary arterial hypertension and those who have pulmonary arterial hypertension due to chronic pulmonary thrombembolism or systemic connective tissue disorders. It is therefore important for personal physicians to think of pulmonary hypertension in the case of suspicious symptoms in the patient's medical history (excessive tiredness, chest pain, tachycardia, dyspnea and syncope upon exertion), so that they can perform a clinical examination and basic tests, and, in case of major clinical suspicion, also refer the patient to an appropriate specialist (pulmologist, cardiologist or rheumatologist) or to an emergency internal medicine office, if the patient's life is acutely endangered.
Summary     Pljučna arterijska hipertenzija je kronična bolezen, ki se pojavlja primarno ali v povezavi z drugimi boleznimi, predvsem s kroničnimi pljučnimi trombembolizmi in sistemskimi boleznimi veziva. Zaradi večanja krvnega tlaka v pljučnem krvotoku pride do desnostranskega srčnega popuščanja in odpovedi desnega srca. Skoraj vedno je povezana s slabim potekom bolezni. Pogosto dolgo ostane neprepoznana, čeprav jo lahko odkrijemo s preprostimi diagnostičnimi postopki, kot so, poleg anamneze in natančnega kliničnega pregleda, še EKG, rentgenska slika prsnega koša in UZ-srca. Nova spoznanja o etiopatogenezi pljučne arterijske hipertenzije odpirajo nove možnosti zdravljenja z zdravili in/ali operativnimi posegi, tako za bolnike s primarno pljučno arterijsko hipertenzijo kot za bolnike s pljučno arterijsko hipertenzijo zaradi kroničnih pljučnih trombembolizmov afi sistemskih bolezni veziva. Zato je pomembno, da ob sumljivih anamnestičnih simptomih (čezmerna utrujenost, bolečine v prsih, tahikardije, dispneja in sinkopa ob obremenitvi) pomisli na pljučno hipertenzijo že osebni zdravnik, opravi klinični pregled, osnovne preiskave in ob velikem kliničnem sumu bolnika ustrezno napoti k specialistu (pulmologu, kardiologu ali revmatologu) oziroma v nujno (urgentno) internistično ambulanto, če je bolnikovo življenje akutno ogroženo.
Descriptors     HYPERTENSION, PULMONARY