Author/Editor | Rode, Matjaž; Groznik, Ignac; Kogoj-Rode, Mirela | |
Title | Spremembe v ustni votlini pri bolnikih s kleidokranialno disostozo - opis primera | |
Translated title | Oral cavity changes in patients with dysostosis cleidocranialis - case report | |
Type | članek | |
Source | Zdrav Vestn | |
Vol. and No. | Letnik 73, št. 11 | |
Publication year | 2004 | |
Volume | str. 815-7 | |
Language | slo | |
Abstract | Background. Dysostosis cleidocranialis (DCC) is a rare systemic disease that can be classified as autosomaldominant hereditary dysplasia and presents with disease characteristical changes in mouth. These can cause severe psychological problems especially in adolescent patients. Conclusions. Orthodontic treatment of the facial sceletal and teeth abnormalities can be problematic in patients with DCC. Therefore, interdisciplinary planned dental/orthodontic rehabilitation is vital. This article presents a rehabilitation method in female patient with DCC. | |
Summary | Izhodišča. Dysostosis cleidocranialis (DCC) je redka sistemska bolezen, ki jo uvrščamo med avtosomno dominantno dedovane displazije in ima poleg ostalih sprememb tudi za bolezen značilne spremembe v ustni votlini. To lahko predvsem v obdobju pubertete privede do hudih duševnih obremenitev. Zaključki. Ortodontsko zdravljenje obraznih skeletnih in zobnih nepravilnosti - disgnatij - je pri bolnikih z DCC težavno. Zato je nujna interdisciplinarno načrtovana stomatoprotetična rehabilitacija. Avtorji so v članku prikazali način rehabilitacije pri bolnici z DCC. | |
Descriptors | CLEIDOCRANIAL DYSPLASIA ORTHODONTICS, CORRECTIVE DENTURE, PARTIAL, REMOVABLE ADULT |