Author/Editor     Vidovič-Valentinčič, Nataša; Brecelj, Jelka; Beltram, Matej; Kraut, Aleksandra
Title     Predstavitev treh slovenskih bolnikov z Vogt-Koyanagi-Haradovo boleznijo
Translated title     Three MB. Vogt-Koyanagi-Harada cases in Slovenia
Type     članek
Source     Zdrav Vestn
Vol. and No.     Letnik 74, št. 10
Publication year     2005
Volume     str. 649-53
Language     slo
Abstract     Background. To describe diagnostic criteria, clinical manifestations and course of disease in patients with Mb. Vogt-Koyanagi-Harada (VKH), examined and treated at the University Eye Clinic in Ljubljana. Patients and methods. We included all patients diagnosed with VKH, who were treated at the University Eye Clinic in Ljubljana. Their history, results of examinations and diagnostic tests as well as the received treatment and outcome were reviewed and compared. Results. We present three patients with VKH, a women and two men, aged 26, 30 and 40 years at time of disease onset. In all cases eye involvement was bilateral, there was no history of penetrating ocular trauma or surgery proceding the initial onset if uveitis, there were no clinical or laboratory evidence suggestive for other uveitic entities. The diagnosis was established on the ground of ocular and systemic signs. Conclusions. VKH is as expected to be a rare disease in Slovenia as it is linked with certain ethnical and racial groups.
Summary     Izhodišča. Opis diagnostičnih meril, kliničnih pojavov in poteka bolezni Vogt-Koyanagi-Harada pri bolnikih, pregledanih in zdravljenih na Očesni kliniki v Ljubljani. Metode. Retrospektivna analiza bolnikov in njihove dokumentacije, pregledanih in zdravljenih na Očesni kliniki v Ljubljani, pri katerih je bil postavljen sum na bolezen Vogt-Koyanagi-Harada. Rezultati. Predstavljeni so trije bolniki z Vogt-Koyanagi-Haradovo boleznijo, ženska in dva moška, ob odkritju bolezni stari 26, 30 in 40 let. Pri vseh bolnikih sta bili prizadeti obe očesi, nobeno oko ni utrpelo penetrantne poškodbe ali znotrajočesne operacije, preden se je pojavilo očesno vnetje, drugi možni vzroki za uveitis so bili izključeni. Diagnoza je bila postavljena na osnovi očesnih in neočesnih znakov. Zaključki. Bolezen Vogt-Koyanagi-Harada v Sloveniji (pričakovano) ni pogosta, saj se značilno povezuje z nekaterimi rasnimi in etničnimi skupinami.
Descriptors     UVEOMENINGOENCEPHALITIC SYNDROME
UVEITIS
FLUORESCEIN ANGIOGRAPHY
MIDDLE AGE
ADULT