Author/Editor		Bervar, Marijan
Title		Protuberantni dermatofibrosarkom - fibrohistiocitni tumor srednje stopnje malignosti
Translated title		Dermatofibrosarcoma protuberans - fibrohistiocytic tumor of intermediate malignancy
Type		članek
Source		In: Vrabič E, editor. Zbornik referatov 50 let Oddelka za plastično in rekonstruktivno kirurgijo; 2005 okt 21; Maribor. Maribor: Splošna bolnišnica Maribor,
Publication year		2005
Volume		str. 249-58
Language		slo
Abstract		Dermatofibrosarcoma protuberans has a high rate of recurrence, presumably as a consequence of persistent residual tumor. This is probably the main reason why repeated surgical treatment is frequently required. In the article we present our experience of surgical treatment of such malignancy on the neck and shoulder in an elder male after twelve years follow-up period. The case is interesting because we started with surgical treatment relatively late in the unfavorable, fully developed stage of the disease, with multiple satellite nodules spreading and signs of partial myxoide degeneration of the largest tumor mass itself. Despite initial wide excision, five local recurrences-fortunately without distant metastases-were observed during the first eight years. The recurrences appeared mostly in the region of greatest tumor degeneration and infiltration and where the excision margins were less than 2 cm apart from the visible tumor mass. A sufficiently wide excision, long-term follow-up and good co-operation between surgeon and experienced pathologist are crucial for the strategy of treatment and the prognosis of this unusual malignancy.
Descriptors		SKIN NEOPLASMS DERMATOFIBROSARCOMA NEOPLASM RECURRENCE, LOCAL REOPERATION AGED