Author/Editor | Kamhi, T; Meglič, A | |
Title | Prirojena posteriorna zaklopka sečnice - pomemben vzrok za kronično ledvično odpoved pri otrocih | |
Translated title | Congenital posterior urethral valve - an important cause of chronic renal failure in children | |
Type | članek | |
Source | Slov Pediatr | |
Vol. and No. | Letnik 13, št. 1 | |
Publication year | 2006 | |
Volume | str. 44-7 | |
Language | slo | |
Abstract | The causes of obstructive nephropathy in early infancy are congenital malformations of the urinary tract that lead to obstruction of urine flow at various levels of the urinary tract. Infants with congenital urethral valves have the least favourable prognosis. They develop chronic renal failure in early childhood and many have micturition disturbances and irreparable urinary incontinence. In this article the clinical characteristics of congenital posterior urethral valves, diagnostic protocol and treatment options are described. Renal function in these children in later years is largely dependent on early recognition and effective treatment in the first days of life. | |
Summary | Razlogi za obstruktivno nefropatijo v dojenčkovem obdobju so prirojene napake sečil, zaradi česar nastane motnja odtoka urina na različnih ravneh sečil. Otroci s prirojeno zaklopko sečnice imajo najslabšo napoved izida. Že v zgodnjem otroštvu razvijejo kronično ledvično odpoved, veliko jih ima motnjo mikcije, in sicer nepopravljivo urinsko inkontinenco. V članku opisujemo klinično sliko prirojene posteriorne zaklopke sečnice, zaporedje preiskav in postopkov zdravljenja. Stanje ledvične funkcije v kasnejših letih je pri teh otrocih v veliki meri odvisno od hitrega prepoznavanja in učinkovitega ukrepanja že v prvih dneh po rojstvu. | |
Descriptors | URETHRAL OBSTRUCTION URETHRA VESICO-URETERAL REFLUX KIDNEY FAILURE, CHRONIC INFANT |