Author/Editor | Skok, Pavel; Knehtl, Maša; Ćeranić, Davorin | |
Title | Neobičajen vzrok usodne krvavitve v trebušno votlino - predstavitev bolnika | |
Type | članek | |
Source | In: Gričar M, Vajd R, editors. Urgentna medicina: izbrana poglavja 2008. Zbornik 15. mednarodni simpozij o urgentni medicini; 2008 jun 11-14; Portorož. Ljubljana: Slovensko združenje za urgentno medicino, | |
Publication year | 2008 | |
Volume | str. 281-3 | |
Language | slo | |
Abstract | Atraumatic splenic rupture and hemorrhage into the abdominal cavity is an extremely unusual and rare complication of internal disease. Hemopathies, inflammatory or infiltrative diseases affecting the spleen are possible causes for such a complication. Splenomegaly is a factor, which may significantly increase the risk of rupture. In the paper the authors are presenting a 52-year patient with an unusual and fatal complication of systemic amyloidosis. Amyloidosis is a disorder of protein metabolism, during which the accumulation of an insoluble protein occurs in the intercellular space of heart, liver, kidneys, spleen, peripheral nerves and other organs. | |
Summary | Atravmatsko raztrganje vranice in izkrvavitev v trebušno votlino je zelo neobičajen in redek zaplet internistične bolezni. Med vzroki, ki lahko vplivajo na tak zaplet so krvne, vnetne ali infiltrativne bolezni, ki prizadenejo vranico. Splenomegalija je dejavnik, ki tveganje za raztrganje organa pomembno poveča. V prispevku avtorji predstavljamo 52-letnega bolnika, pri katerem smo ugotovili sistemsko amiloidozo, ki je bila vzrok usodnega zapleta. Amiloidoza je motnja presnove beljakovin, ki se razvije pri različnih obolenjih in pri kateri se v medceličnini srca, jeter, ledvic, vranice, perifernih živcev ali drugih organov odlaga netopna beljakovina. | |
Descriptors | SPLENIC RUPTURE GASTROINTESTINAL HEMORRHAGE AMYLOIDOSIS |