Author/Editor		Borinc-Beden, Andreja; Brecelj, Jernej; Bratanič, Nina; Homan, Matjaž; Homšak, Matjaž; Jenko, Klemen; Kenig, Anton; Oštir, Majda; Skočir, Lidija; Širca-Čampa, Andreja
Title		Smernice za obravnavo otrok s cistično fibrozo
Translated title		Guidelines for management of children with cystic fibros
Type		članek
Source		Zdrav Vestn
Vol. and No.		Letnik 77, št. 10
Publication year		2008
Volume		str. 679-92
Language		slo
Abstract		Cystic fibrosis is the most common autosomal recessive hereditary disease. The clinical consequences include multisystem disease characterised by progressive pulmonary disease leading to respiratory failure, pancreatic disfunction, liver disease that may progress to chirrhosis and men infertility due to atresia of the vas deferens. Early intervention and prevention of lung disease is of paramount importance, since the prognosis of the disease is substantially dependent on chronic respiratory infection and inflammation. Cystic fibrosis is a complex disease requiring a multidisciplinary approach to treatment. Center care by a team of experienced health professionals is essential for optimal patient management and outcome.
Descriptors		CYSTIC FIBROSIS PRACTICE GUIDELINES CHILD