Author/Editor     Dolenc, Jure; Zver, Samo; Koželj, Mirta; Fink, Martina; Pajič, Tadej
Title     Ebsteinova anomalija z redko motnjo strjevanja krvi ‐ Prikaz primera in pregled literature
Translated title     Ebstein's anomaly and a rare coagulation disorder ‐ Case report and review of literature
Type     članek
Source     Zdrav Vestn
Vol. and No.     Letnik 78, št. 10
Publication year     2009
Volume     str. 576-80
Language     slo
Abstract     Backgrounds: Ebstein’s anomaly of tricuspid valve is a rare congenital heart anomaly. Surgical implantation of artei cial tricuspid valve is a standard treatment modality. Common late complication of such surgical procedure is artei cial valve thrombosis. h is is a life threatening condition, which demands surgical intervention promptly. Conclusions: In following article, we describe a case of a patient with Ebstein’s anomaly and late artei cial tricuspid valve thrombosis. The case was complicated with a mild form of haemophilia C, a rare coagulation disorder. Genetic analysis was also performed.
Descriptors     EBSTEIN'S ANOMALY
FACTOR XI DEFICIENCY
HEART VALVE PROSTHESIS
POSTOPERATIVE COMPLICATIONS
THROMBOSIS
ADULT
ECHOCARDIOGRAPHY, DOPPLER, COLOR