Author/Editor | Majal, Maja; Hauptman, Jasmina | |
Title | Primarna mielofibroza | |
Translated title | Primary myelofibrosis | |
Type | članek | |
Source | In: Hojs R, Krajnc I, Pahor A, et al, editors. Zbornik predavanj in praktikum 21. srečanje internistov in zdravnikov družinske medicine Iz prakse za prakso z mednarodno udeležbo; 2010 maj 28-29; Maribor. Maribor: Univerzitetni klinični center, Klinika za interno medicino, | |
Publication year | 2010 | |
Volume | str. 77-83 | |
Language | slo | |
Abstract | Primary myelofibrosis is clonal myeloproliferative disease characterized by marrow fibrosis, myeloid dysplasia with extramedullary hematopoesis and splenomegaly. Most patients present with anemia and splenomegaly. The peripheral blood smear shows dacrocytes and leukoerytroblastic blood picture. Supportive therapy is generally used. | |
Summary | Primarna mielofibroza je klonska mieloproliferativna bolezen, za katero je značilna fibroza kostnega mozga, mieloidna metaplazija z ekstramedularno hematopoezo in splenomegalija. V klinični sliki so v ospredju znaki anemije in splenomegalije. Značilne so spremembe v diferencialni krvni sliki z dakriociti in levkoeritroblastozo. Zdravljenje je v večini primerov simptomatsko. | |
Descriptors | ANEMIA SPLENOMEGALY |