Author/Editor		Ravnik, Janez; Potrč, Stojan; Kavalar, Rajko; Ravnik, Maja; Zakotnik, Branko; Bunc, Gorazd
Title		Dumbbell synovial sarcoma of the thoracolumbar spine
Type		članek
Vol. and No.		Letnik 34, št. 10
Publication year		2009
Volume		str. E363-E366
ISSN		0362-2436 - Spine
Language		eng
Abstract		Study design. A case report is of a giant dumbbell-shaped synovial sarcoma of the thoracolumbar spine is presented. Objective. To report a case of a rare dumbbell-shaped tumor treated by multimodal approach. Surgical procedures, adjuvant treatment, and outcome were discussed. Summary of background data. Synovial sarcomas of the spine are very rare tumors. Radical surgical resection is the goal, but is often not feasible. Dumbbell-shaped spinal synovial sarcoma with a giant extraspinal extension has not yet been reported. The rationale for 2-step surgical procedure and adjuvant therapy is discussed in light of the clinical picture, preoperative imaging and extension of the disease. Methods. A 32-year-old male patient presented with signs of quickly progressive paraparesis. A dumbbell-shaped tumor at the levelTh12-L1 was found with a giant retroperitoneal extension. Tumor was nonradically excised in a 2-step operation: first through a dorsal approach with laminectomy and removal of the intraspinal extradural part, and later through a laparotomy with removal of the retroperitoneal part. Histologic examination revealed highly malignant synovial sarcoma. Patient was treated with chemotherapy and radiotherapy after surgery. Results. Patient was in remission and symptom free for 1 year after surgery; he then developed a local recurrence and died soon afterwards. Conclusion. A good treatment result was achieved initially. A combined approach in cases like this is warranted, with as radical surgery as possible in order to avoid local recurrence, a common cause of treatment failure in sarcomas.
Descriptors		Sarcoma, Synovial Sinovialni sarkom Spinal Neoplasms Spinalne novotvorbe Retroperitoneal Neoplasms Retroperitonealne novotvorbe Surgical Procedures, Operative Kirurški postopki, operativni Chemotherapy, Adjuvant Kemoterapija, pomožna Radiotherapy Radioterapija diagnosis therapy surgery Diagnostika Zdravljenje Kirurgija