Author/Editor     Zorn, Branko
Title     Sindrom HELLP - patofiziologija, diagnostika in zdravljenje
Translated title     HELLP syndrome: pathophysiology, diagnosis and therapy
Type     članek
Source     Zdrav Vestn
Vol. and No.     Letnik 67, št. 7-8
Publication year     1998
Volume     str. 405-10
Language     slo
Abstract     Background. HELLP syndrome, characterized by association of hemolysis, elevated liver enzymes, and low platelets, is a severe form of pre-eclampsia. Materials and methods. The author reports a case of a 34-year old primigravida who complained of an epigastric pain with all signs of pre-eclampsia at the 32nd week of gestation; a caeserean delivery was urgently performed. Conclusions. Discussion was made upon the prevalence, the biological and clinical features, the pathophysiology, the risk factors and therapy of the HELLP syndrome. Both rapid termination of pregnancy or conservative approach require permanent multidisciplinary materno-fetal follow-up.
Summary     Izhodišča. Sindrom HELLP (H-hemolysis, EL-elevated liver enzymes, PL-low platelets) je posebna oblika preeklampsije. Materiali in metode. Prikazan je primer omenjenega sindroma pri prvesnici v 32. tednu nosečnosti s prevladujočim kliničnim simptomom epigastrične bolečine in vsemi znaki preeklampsije. Narejen je bil urgentni carski rez. V prispevku so prikazani: pogostnost tega sindroma, laboratorijsko značilni znakiin klinična slika, patofiziologija, dejavniki tveganja za razvoj sindroma in zdravljenje. Zaključki. Klinični prikaz in teoretični vidiki so dokaz o pomembnosti sindroma HELLP. Tako hitra prekinitev nosečnosti, kot tudi konservativno zdravljenje zahtevata stalno multidiscplinarno obravnavo matere in ploda.
Descriptors     HELLP SYNDROME
PREGNANCY
PRE-ECLAMPSIA