Author/Editor | Lužnik-Bufon, Tatjana | |
Title | Prirojene pomanjkljivosti komplementa | |
Translated title | Inherited complement deficiencies | |
Type | članek | |
Source | Med Razgl | |
Vol. and No. | Letnik 37, št. Suppl 5 | |
Publication year | 1998 | |
Volume | str. 131-5 | |
Language | slo | |
Abstract | The development of avious assay technologies and genetics has resulted in a number of clinical conditions in which the complement is implicated. For many countries, clinical "complementology" is entering into an exciting phase. The advances in the field of study of the complement system and its control are beginning to be applied in clinical settings. In three patients from 2 to 11 years old, hospitalised in our department, with meningococcal infections, we diagnosed complement deficiency of some components - C2, C7 and C8. | |
Summary | Razvoj preiskovalnih tehnik, ki merijo dejavnost in količino sestavin komplementnega sistema, in genetike je omogočil prepoznavanje različnih kliničnih dogajanj, v katera je vpleten komplement. Klinična "komplementologija" je v mnogih držazah v obdobju dinamičnega razvoja. Nova dogajanja na področju komplementnega sistema in nadzora ponovno pridobivajo mesto v klinični obravnavi bolnika. Pri treh bolnikih, starih 2 do 11 let, ki so ležali na naši kliniki zaradi meningokokne okužbe, smo ugotovili pomanjkanje določenih komponent komplementa - C2, C7 in C8. | |
Descriptors | COMPLEMENT COMPLEMENT PATHWAY, ALTERNATIVE COMPLEMENT PATHWAY, CLASSICAL |