Author/Editor     Lužnik-Bufon, Tatjana
Title     Prirojene pomanjkljivosti komplementa
Translated title     Inherited complement deficiencies
Type     članek
Source     Med Razgl
Vol. and No.     Letnik 37, št. Suppl 5
Publication year     1998
Volume     str. 131-5
Language     slo
Abstract     The development of avious assay technologies and genetics has resulted in a number of clinical conditions in which the complement is implicated. For many countries, clinical "complementology" is entering into an exciting phase. The advances in the field of study of the complement system and its control are beginning to be applied in clinical settings. In three patients from 2 to 11 years old, hospitalised in our department, with meningococcal infections, we diagnosed complement deficiency of some components - C2, C7 and C8.
Summary     Razvoj preiskovalnih tehnik, ki merijo dejavnost in količino sestavin komplementnega sistema, in genetike je omogočil prepoznavanje različnih kliničnih dogajanj, v katera je vpleten komplement. Klinična "komplementologija" je v mnogih držazah v obdobju dinamičnega razvoja. Nova dogajanja na področju komplementnega sistema in nadzora ponovno pridobivajo mesto v klinični obravnavi bolnika. Pri treh bolnikih, starih 2 do 11 let, ki so ležali na naši kliniki zaradi meningokokne okužbe, smo ugotovili pomanjkanje določenih komponent komplementa - C2, C7 in C8.
Descriptors     COMPLEMENT
COMPLEMENT PATHWAY, ALTERNATIVE
COMPLEMENT PATHWAY, CLASSICAL