| Author/Editor | Kitano, Y | |
| Title | Juvenile hyaline fibromatosis | |
| Type | članek | |
| Source | Acta Dermatovenerol Alp Pannon Adriat | |
| Vol. and No. | Letnik 8, št. 1 | |
| Publication year | 1999 | |
| Volume | str. 5-11 | |
| Language | eng | |
| Abstract | Juvenile hyaline fibromatosis is a rare congenital disease with characteristic clinical and histopathological features. Clinical symptoms develop early in life, ranging from one month ro four years of age. Tumors and nodules are most outstanding symptoms. Whitish papules, hyperthropy of the gingiva and flexural contracture of joints are the essential symptoms. X-ray extamination often reveals osteolytic or destructive bone lesions. Histopathology shows abundant deposition of hyaline substance in the tumor. In most cases, those main symptoms are not directly life-threatening, but ultimate prognosis is poor. | |
| Descriptors | FIBROMA HYALIN NEOPLASMS, FIBROUS TISSUE GINGIVAL HYPERTROPHY CONTRACTURE JOINTS OSTEOLYSIS |