Author/Editor     Potušek-Kuhar, K; Logar-Car, G; Mlinarič, V
Title     Primarni sklerozirajoči holangitis pri otroku
Translated title     Primary sclerosing cholangitis at the children
Type     članek
Source     Slov Pediatr
Vol. and No.     Letnik 4, št. 3-4
Publication year     1997
Volume     str. 54-6
Language     slo
Abstract     The article describes the patient with sclerosing cholangitis as well as chronic inflammatory bowel disease. The epidemiology, pathogenesis, clinical picture, diagnostics, prognosis and treatment of the disease are described. A 13-year boy was diagnosed to have chronic inflammatory bowel disease. Because of recuring pathological liver tests and increased direct bilirubin the sclerosing cholangitis was suspected. Endoscopic retrograde cholangiopancreatography confirmed the diagnosis. The treatment included ursodeoxycholic acid which normalized liver tests.
Summary     Članek prikazuje bolnika s sklerozirajočim holangitisom, ki ima hkrati tudi kronično vnetno črevesno bolezen. Opisuje epidemiologijo, patogenezo, klinično sliko, prognozo in zdravljenje bolezni. Pri bolniku smo v starosti 13 let diagnosticirali kronično vnetno črevesno bolezen. Zaradi ponavljajočih se povišanih vrednosti jetrnih testov in direktnega bilirubina smo posumili na sklerozirajoči holangitis. Opravili smo endoskopsko retrogradno holangiopankreatografijo, ki je diagnozo potrdila. V zdravljenje smo vključili ursodeoksiholno kislino in jetrni testi so se normalizirali.
Descriptors     CHOLANGITIS, SCLEROSING
INFLAMMATORY BOWEL DISEASES
CHILD