Author/Editor		Flis, Vojko; Pavlovič, Milan; Matela, Jože
Title		Kronična venska insuficienca in kongenitalne anomalije
Translated title		Chronic venous insufficiency and congenital anomalies
Type		članek
Source		Med Razgl
Vol. and No.		Letnik 39, št. Suppl 2
Publication year		2000
Volume		str. 129-33
Language		slo
Abstract		Chronic venous insufficiency accompanies a rare congenital and generalised mesodermal abnormality, called the Klippel-Trenaunay syndrome, which is characterised by macular vascular nevi, skeletal or soft tissue hypertrophy and venous varicosities. Other associated manifestations include deep venous anomalies, arteriovenous microfistulae, visceral hemangiomas and the Kasabach Merritt syndrome. In the related Parkes-Weber syndrome, high-output cardiac failure with macroarteriovenous fistula is frequently seen. Two patients with the Parkes-Weber and Klippel-Trenaunay syndrome are presented and their clinical pictures are reviewed.
Summary		Kronična venska insuficienca je spremljevalka redke prirojene bolezni mezoderma, za katero so značilni kožni hemangiomi, hipertrofija skeleta ali mehkih tkiv in varikozne vene. Gre za sindrom Klippel-Trenaunay. Pri bolnikih s to boleznijo lahko najdemo tudi anomalije na globokih venah, arterio-venske mikrofistule. Pogosto pa jo spremlja tudi sindrom Kasabach-Merrit. Pri sorodnem sindromu Parkes-Weber pogostokrat srečamo odpovedovanje srca in pojavljanje arterio-venskih makrofistul. Predstavljena sta bolnika s Parkes-Weberjevim sindromom in s sindromom Klippel-Trenaunay.
Descriptors		VENOUS INSUFFICIENCY VEINS CHRONIC DISEASE KLIPPEL-TRENAUNAY-WEBER SYNDROME ARTERIOVENOUS FISTULA HEMANGIOMA DIAGNOSIS, DIFFERENTIAL