Author/Editor | Glaser, Marjana | |
Title | Krioglobulinemija pri kronični limfocitni levkemiji | |
Translated title | Cryoglobulinemia in chronic lymphocytic leukemia | |
Type | članek | |
Source | Med Razgl | |
Vol. and No. | Letnik 39, št. Suppl 5 | |
Publication year | 2000 | |
Volume | str. 133-7 | |
Language | slo | |
Abstract | Cryoglobulinemia is a symptom, accompanying various infectious or autoimmune diseases and cancers, but it is rare described in B cell chronic lymphocytic leukemia (B CLL). Hyperviscosity syndrome and organ tissue damage are the consequence of cryoglobulin in blood and deposition in blood and in vessel wall, which affects especially skin, nervous system, kidney and liver. Treatment of choice are plasmapheresis and chemotherapy. In this paper two patients with C KLL and hyperviscosity syndrome are described. | |
Summary | Krioglobulinemija je simptom, ki spremlja različne vnetne, avtoimune in rakaste bolezni, redkeje je opisana pri kronični limfocitni levkemiji (B KLL). Zaradi kopičenja krioglobulinov v krvnem obtoku in njihovega nalaganja v žilah se pojavijo znaki hiperviskoznosti in poškodbe organskih sistemov, ki prizadenejo predvsem kožo, živčevje, ledvice in jetra. Zdravimo s plazmaferezo in s citostatiki. V sestavku sta predstavljena dva bolnika z napredovalo B KLL in znaki hiperviskoznega sindroma. | |
Descriptors | LEUKEMIA, B-CELL, CHRONIC CRYOGLOBULINEMIA MIDDLE AGE AGED |