Author/Editor     Černelč, Peter
Title     Prikaz bolnice s pridobljeno hemofilijo A in tremi drugimi imunskimi obolenji
Translated title     Patient with acquired hemophilia A and three other immune disease
Type     članek
Source     Med Razgl
Vol. and No.     Letnik 39, št. Suppl 5
Publication year     2000
Volume     str. 157-160
Language     slo
Abstract     Bleeding in acquired hemophilia A patients with F VIII autoantibodies is often severe, lifethreatening and refractory to treatment with factor VIII concentrates. In this report, we describe an elderly woman with acquired hemophilia A with FVIII autoantibodies and three other immune diseases (vasculitis, chronic thyroiditis, idiopathic thrombocytopenic purpura). The treatment of bleeding with activated prothrombin copmlex (FEIBA) concentrates was efficacy several times without complications.
Summary     Pri pridobljeni hemofiliji A zaradi protiteles proti F VIII so krvavitve pogosto obsežne, ki bolnika ogrožajo. Zdravljenje s koncentrati faktorja VIII je neučinkovito. Prikazujemo starejšo bolnico s pridobljeno hemofilijo A zaradi protiteles proti F VIII in tremi drugimi imunskimi boleznimi (vaskulitis, kronični tiroiditis, idiopatična trombocitopenična purpura). Zdravljenje večjih krvavitev s koncentratom aktiviranega protrombinskega kompleksa (FEIBA) je bilo večkrat učinkovito. Zapletov med zdravljenjem ni bilo.
Descriptors     HEMOPHILIA
FACTOR VIII
AGED
THYROIDITIS, AUTOIMMUNE
PURPURA, THROMBOCYTOPENIC, IDIOPATHIC
VASCULITIS
TREATMENT OUTCOME