Author/Editor | Černelč, Peter | |
Title | Prikaz bolnice s pridobljeno hemofilijo A in tremi drugimi imunskimi obolenji | |
Translated title | Patient with acquired hemophilia A and three other immune disease | |
Type | članek | |
Source | Med Razgl | |
Vol. and No. | Letnik 39, št. Suppl 5 | |
Publication year | 2000 | |
Volume | str. 157-160 | |
Language | slo | |
Abstract | Bleeding in acquired hemophilia A patients with F VIII autoantibodies is often severe, lifethreatening and refractory to treatment with factor VIII concentrates. In this report, we describe an elderly woman with acquired hemophilia A with FVIII autoantibodies and three other immune diseases (vasculitis, chronic thyroiditis, idiopathic thrombocytopenic purpura). The treatment of bleeding with activated prothrombin copmlex (FEIBA) concentrates was efficacy several times without complications. | |
Summary | Pri pridobljeni hemofiliji A zaradi protiteles proti F VIII so krvavitve pogosto obsežne, ki bolnika ogrožajo. Zdravljenje s koncentrati faktorja VIII je neučinkovito. Prikazujemo starejšo bolnico s pridobljeno hemofilijo A zaradi protiteles proti F VIII in tremi drugimi imunskimi boleznimi (vaskulitis, kronični tiroiditis, idiopatična trombocitopenična purpura). Zdravljenje večjih krvavitev s koncentratom aktiviranega protrombinskega kompleksa (FEIBA) je bilo večkrat učinkovito. Zapletov med zdravljenjem ni bilo. | |
Descriptors | HEMOPHILIA FACTOR VIII AGED THYROIDITIS, AUTOIMMUNE PURPURA, THROMBOCYTOPENIC, IDIOPATHIC VASCULITIS TREATMENT OUTCOME |