Author/Editor     Sabolić, Josip; Klemenc, Matjaž; Košuljandić, Velimir
Title     Primarni fibrosarkom srca
Translated title     Primary fibrosarcoma of the heart
Type     članek
Source     Zdrav Vestn
Vol. and No.     Letnik 70, št. 11
Publication year     2001
Volume     str. 643-6
Language     slo
Abstract     Background. Primary tumors of the heart are rare, with an incidence between 0.0017 and 0.27 in reported or collected autopsy series. Near 30% of primary tumors are malignant, among them sarcomas are most frequent. Clinical symptoms are nonspecific: signs of congestive heart failure, chest pain, cough, weakness. Echocardiography is still cornerstone of noninvasive detection of cardiac tumors; other diagnostic techniques are computerized axial tomography and nuclear magnetic resonance. Surgical resection of tumor is the most important way of the treatment of primary malignant cardiac tumors. Conclusions. In this case report authors describe a 55 years old man with echocardiographicaly diagnosed cardiac tumor. Later, tumor was more precisely assessed by computerized tomography and nuclear magnetic resonance. Because of progression of the tumor and involvement of coronary vessels, the tumor was not suitable for surgical resection. At autopsy, a primary fibrosarcoma of the heart was confirmed.
Summary     Izhodišča. Primarni tumorji srca so izrazito redki, ocenjena incidenca v različnih serijah avtopsij se giblje med 0,0017 in 0,23%. Približno 30% teh tumorjev je malignih, med njimi so najpogostejši sarkomi. Bolniki največkrat pridejo k zdravniku zaradi znakov srčnega popuščanja, bolečin v prsnem košu, kašlja, slabega počutja. Ultrazvočna preiskava srca je osnovna diagnostična metoda, dopolnjujejo jo računalniška tomografija, magnetna resonanca in invazivne preiskave srca. Kirurška odstranitev tumorja predstavlja temelj zdravljenja. Preživetje po odkritju primarnega malignega tumorja srca je razmeroma kratko, pa delni resekciji primarnega sarkoma srca do 6 mesecev. Zaključki. V prispevku avtorji opisujejo primer 55-letnega bolnika, pri katerem je bil z ultrazvočno preiskavo ugotovljen tumor v steni levega preddvora, kasneje natančneje opisan s pomočjo računialniške tamografije in magnetne resonance. Zaradi obsežnosti tumorja in zajetja venčnih arterij operativni poseg ni bil možen, kasneje je obdukcija pokazala, da je v opisanem primeru šlo za primarni fibrosarkom srca.
Descriptors     HEART NEOPLASMS
FIBROSARCOMA
MIDDLE AGE
ECHOCARDIOGRAPHY
THORACIC RADIOGRAPHY