Author/Editor | Anderluh, F; Sedmak, M; Kenig, T; Strlič, M | |
Title | Prirojene anomalije anorektalnega področja | |
Translated title | Congenital anorectal anomalies | |
Type | članek | |
Source | Slov Pediatr | |
Vol. and No. | Letnik 9, št. 1 | |
Publication year | 2002 | |
Volume | str. 12-6 | |
Language | slo | |
Abstract | Congenital anorectal anomalies are rare anomalies presented soon after birth with the complications of defecation. They can be associated with the anomalies of other organs. Classification by low, intermediate and high anomalies is based on the anatomy. The diagnosis is confirmed with the clinical examination and imaging techniques. The therapy consists of surgical correction of anomalies. The prognosis depends on severity of both anorectal and associated anomalies. A nine-weeks-old girl with rectovaginal - vestibular fistula is presented. The diagnosis was confirmed with irigography after the suspicion based on clinical examination. The anomaly was surgically corrected. | |
Summary | Prirojene anomalije anorektalnega področja so razmeroma redke anomalije, ki se običajno pokažejo kmalu po rojstvu s težavami pri odvajanju blata. Lahko so združene z anomalijami drugih organskih sistemov. Glede na anatomske razmere jih delimo na nizke, intermediarne in visoke. Za postavitev osnovne diagnoze in prikaz morebitnih pridruženih anomalij so pomembni klinični pregled in slikovne diagnostične metode. Zdravljenje je kirurško, prognoza pa je odvisna od kompleksnosti anorektalne in pridruženih anomalij. V prispevku je opisana deklica, stara devet tednov, ki je bila napotena na Pediatrično kliniko zaradi tri tedne trajajoče hematohezije in perzistentno povišane sedimentacije. Ob kliničnem pregledu je bil postavljen sum na rektovaginalno fistulo, ki je bila potrjena z irigografijo in kirurško oskrbljena. | |
Descriptors | ANUS RECTUM RECTOVAGINAL FISTULA INFANT |