Author/Editor     Ravnik, Janez; Podlesnik, Maja; Markovič, Saša; Koželj, Mirta
Title     Ehokardiografska diagnostika karcinoidne srčne bolezni
Translated title     Echocardiographic diagnostics of carcinoid heart disease
Type     članek
Source     Zdrav Vestn
Vol. and No.     Letnik 71, št. 9
Publication year     2002
Volume     str. 529-33
Language     slo
Abstract     Background. Carcinoid heart disease is a rare heart disease which affects endocard and heart valves on the right side of heart. It affects only patients with manifested carcinoid syndrome, which is thought to be the consequence of secret or active metastases of carcinoid tumour The carcinoid endocardial plaques cause structural changes of tricuspid and pulmonic valve and later on thei rstenosis and/or insufficiency. Patients and methods. In this article we introduce a carcinoid valve heart disease (CVHD) scoring system for easier end exact ehocardiographic diagnostics. Four echocardiographic parameters are beeing estimated: structural changes of tricuspid valve, tricuspid valve regurgitation, stenosis of pulmonic valve and pulmonic valve regurgitation. Conclusions. The scoring system allows us to make an early diagnosis and evaluation of progression of carcinoid heart disease, which is very important for planning the treatment process. Our experiences confirm the usefulness of this scoring system in echocardiographic follow-up of patients with carcinoid syndrome.
Summary     Izhodišča. Karcinoidna srčna bolezen je redka bolezen, ki prizadene endokard in srčne zaklopke desne strani srca. Nanjo moramo pomisliti pri bolnikih z izraženim karcinoidnim sindromom, ki je posledica sekretorne aktivnosti metastaz karcinoidnega tumorja. Zaradi nastanka karcinoidnih leh pride do strukturnih sprememb trikuspidalne in pulmonalne zaklopke ter posledično njune stenoze in/ali insuficience. Bolniki in metode. Za ehokardiografsko ocenjevanje teh sprememb v članku podrobno predstavimo mednarodno uve javjen točkovni sistem (carcinoid valvular heartdisease - CVHD), ki se je tudi pri našem vodenju teh bolnikov izkazal za uporabnega. Ocenjujejo se štirje ehokardiografski parametri: strukturna spremenjenost trikuspidalne zaklopke, regurgitacija trikuspidalne zaklopke, stenoza pulmonalne zaklopke in regurgitacija pulmonalne zaklopke. Zaključki. Točkovni sistem omogoča zgodnjo diagnostiko in vrednotenje napredovanja bolezni, kar je zlasti pomembno za načrtovanje ustreznih terapevtskih ukrepov. Njegovo uporabnost potrjujejo tudi naše izkušnje pri ehokardiografskem spremljanju bolnikov s karcinoidnim sindromom.
Descriptors     CARCINOID HEART DISEASE
ECHOCARDIOGRAPHY
DISEASE PROGRESSION
DIAGNOSIS, DIFFERENTIAL